MTHFR

MEDIUM

Methylenetetrahydrofolate reductase

Chromosome: 1p36.22

Gene Overview

MTHFR encodes methylenetetrahydrofolate reductase, which converts 5,10-methylenetetrahydrofolate to 5-methyltetrahydrofolate, the methyl donor for homocysteine remethylation. The C677T variant (rs1801133) reduces enzyme activity and raises homocysteine, especially when folate intake is low. Associated with cardiovascular disease, neural tube defects, and (controversially) depression. Folate and B-vitamin status are key environmental modifiers; gene–nutrient interactions are well documented.

Molecular Function

  • folate metabolism
  • homocysteine remethylation
  • one-carbon metabolism

Protein class: oxidoreductase

Regulatory Annotation

Promoter activity: Constitutively expressed; nutrient-sensitive.

eQTL tissues: liver, blood

Tissue Expression Context

liverTPM range: 15-40GTEx vv8

Pathways

No pathways linked.

Linked Diseases & Exposures

Diseases

Exposures

Mechanistic Hypotheses

TT genotype increases homocysteine; low folate intake amplifies the effect and cardiovascular risk.

Meta-analyses; folate fortification studies.

MEDIUM

Confidence Rating

Overall evidence confidence for this gene entry: MEDIUM

References

  1. 1.Clarke R, et al. (2012). MTHFR 677C>T and cardiovascular disease. Journal of the American Medical Association. doi:10.1001/jama.2012.1058